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Indian J Pathol Microbiol ; 2007 Apr; 50(2): 329-31
Article in English | IMSEAR | ID: sea-73341

ABSTRACT

Juvenile hyalinefibromatosis (JHF) is a rare autosomal recessive (4q21) genodermatosis characterized by a triad of cephalic fibrous outgrowths, gingival hypertrophy and flexion contractures. This paper presents a case report of juvenile hyaline fibromatosis.


Subject(s)
Child, Preschool , Diagnosis, Differential , Fibroma/diagnosis , Fibromatosis, Aggressive/diagnosis , Fibromatosis, Gingival/diagnosis , Genes, Recessive , Humans , Male , Skin Diseases/diagnosis
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